Mitochondrial Dysfunction in Lysosomal Storage Disorders
نویسندگان
چکیده
منابع مشابه
Mitochondrial Dysfunction in Lysosomal Storage Disorders
Lysosomal storage diseases (LSDs) describe a heterogeneous group of rare inherited metabolic disorders that result from the absence or loss of function of lysosomal hydrolases or transporters, resulting in the progressive accumulation of undigested material in lysosomes. The accumulation of substances affects the function of lysosomes and other organelles, resulting in secondary alterations suc...
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ژورنال
عنوان ژورنال: Diseases
سال: 2016
ISSN: 2079-9721
DOI: 10.3390/diseases4040031